{"product_id":"ass1-polyclonal-antibody-e-ab-52452","title":"ASS1 Polyclonal Antibody - E-AB-52452","description":"\u003cp\u003eASS1 Polyclonal Antibody\u003c\/p\u003e\n\n\u003cp\u003eSizes: 60μL, 120μL, 200μL\u003c\/p\u003e\n\n\u003cp\u003eCatalogue Numbers: E-AB-52452-60, E-AB-52452-120, E-AB-52452-200\u003c\/p\u003e\n\n\u003cp\u003eCitations, Manuals and MSDS Available upon request.\u003c\/p\u003e\n\n\u003cp\u003eAbbreviation: ASS1\u003c\/p\u003e\n\n\u003cp\u003eTarget Synonym: Argininosuccinate synthase 1; Argininosuccinate synthase; Argininosuccinate synthetase 1; ASS; Ass-1; ass1; ASSA; ASSY; Citrulline aspartate ligase; Citrulline--aspartate ligase; CTLN1\u003c\/p\u003e\n\n\u003cp\u003eResearch Areas: Cancer, Metabolism, Signal Transduction\u003c\/p\u003e\n\n\u003cp\u003eConjugation: Unconjugated\u003c\/p\u003e\n\n\u003cp\u003eHost: Rabbit\u003c\/p\u003e\n\n\u003cp\u003eSpecies Reactivity: Human, Mouse, Rat\u003c\/p\u003e\n\n\u003cp\u003eApplication: WB, ELISA\u003c\/p\u003e\n\n\u003cp\u003eIsotype: IgG\u003c\/p\u003e\n\n\u003cp\u003eClonality: Polyclonal\u003c\/p\u003e\n\n\u003cp\u003eUNIProt ID: P00966\u003c\/p\u003e\n\n\u003cp\u003eBackground: ASS1 is a rate-limiting enzyme in the urea cycle. Citrullinemia type I is an autosomal recessive disorder that is caused by a deficiency of the urea cycle enzyme argininosuccinate synthetase (ASS1). Deficiency of ASS1 shows various clinical manifestations encompassing severely affected patients with fatal neonatal hyperammonemia as well as asymptomatic individuals with only a biochemical phenotype.\u003c\/p\u003e\n\n\u003cp\u003eConcentration: 0.4 mg\/mL\u003c\/p\u003e\n\n\u003cp\u003eImmunogen: Fusion protein of human ASS1\u003c\/p\u003e\n\n\u003cp\u003eBuffer: PBS with 0.05% NaN3 and 40% Glycerol, pH7.4\u003c\/p\u003e\n\n\u003cp\u003ePurification Method: Antigen affinity purification\u003c\/p\u003e\n\n\u003cp\u003eDilution: WB 1:500-1:2000, ELISA 1:5000-1:10000\u003c\/p\u003e\n\n\u003cp\u003eCalculated MW: 47 kDa\u003c\/p\u003e\n\n\u003cp\u003eStorage: -20°C\/One year. Avoid freeze \/ thaw cycles.\u003c\/p\u003e\n\n\u003cp\u003eShipping: Ice bag\u003c\/p\u003e\n\n\u003cp\u003eResearch Use Only\u003c\/p\u003e","brand":"Elabscience","offers":[{"title":"60μL","offer_id":43143956594867,"sku":"E-AB-52452-60","price":200.2,"currency_code":"CAD","in_stock":true},{"title":"120μL","offer_id":43143956627635,"sku":"E-AB-52452-120","price":336.0,"currency_code":"CAD","in_stock":true},{"title":"200μL","offer_id":43143956660403,"sku":"E-AB-52452-200","price":558.6,"currency_code":"CAD","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0305\/9482\/6376\/products\/logo_new_c432c496-4a9c-4fc8-858c-8d8d776bed3a.png?v=1710244330","url":"https:\/\/afsbio.com\/products\/ass1-polyclonal-antibody-e-ab-52452","provider":"AFSBio Inc.","version":"1.0","type":"link"}