{"product_id":"etfa-monoclonal-antibody-bt-mca2018","title":"ETFA Monoclonal Antibody - BT-MCA2018","description":"\u003cp\u003eETFA Monoclonal Antibody\u003c\/p\u003e\n\n\u003cp\u003eSizes: 50μL, 100μL\u003c\/p\u003e\n\n\u003cp\u003eCatalogue Number: BT-MCA2018-50, BT-MCA2018-100\u003c\/p\u003e\n\n\u003cp\u003eCitations, Manuals and MSDS Available upon request.\u003c\/p\u003e\n\n\u003cp\u003eBackground: ETFA participates in catalyzing the initial step of the mitochondrial fatty acid beta-oxidation. It shuttles electrons between primary flavoprotein dehydrogenases and the membrane-bound electron transfer flavoprotein ubiquinone oxidoreductase. Defects in electron-transfer-flavoprotein have been implicated in type II glutaricaciduria in which multiple acyl-CoA dehydrogenase deficiencies result in large excretion of glutaric, lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]\u003c\/p\u003e\n\n\u003cp\u003eResearch Areas: Others\u003c\/p\u003e\n\n\u003cp\u003eTarget Protein: ETFA\u003c\/p\u003e\n\n\u003cp\u003eApplications: WB, IHC, FCM\u003c\/p\u003e\n\n\u003cp\u003eClonality: Monoclonal\u003c\/p\u003e\n\n\u003cp\u003eClone ID: 7C2A11\u003c\/p\u003e\n\n\u003cp\u003eHost: Mouse\u003c\/p\u003e\n\n\u003cp\u003eIsotype: Mouse IgG1\u003c\/p\u003e\n\n\u003cp\u003eFull Product Name: ETFA\u003c\/p\u003e\n\n\u003cp\u003eImmunogen: Purified recombinant fragment of human ETFA (AA: 134-333) expressed in E. Coli.\u003c\/p\u003e\n\n\u003cp\u003eStorage: 4°C|-20°C for long term storage\u003c\/p\u003e\n\n\u003cp\u003eFormulation: Purified antibody in PBS with 0.05% sodium azide\u003c\/p\u003e\n\n\u003cp\u003eMolecular Weight (Da): 35kDa\u003c\/p\u003e\n\n\u003cp\u003eUniProt Accession: P13804\u003c\/p\u003e\n\n\u003cp\u003eSynonyms: EMA, GA2, MADD\u003c\/p\u003e\n\n\u003cp\u003eGeneID: 2108\u003c\/p\u003e\n\n\u003cp\u003eResearch Use Only\u003c\/p\u003e","brand":"BT Lab","offers":[{"title":"50μL","offer_id":45238381248691,"sku":"BT-MCA2018-50","price":308.0,"currency_code":"CAD","in_stock":true},{"title":"100μL","offer_id":45238381281459,"sku":"BT-MCA2018-100","price":448.0,"currency_code":"CAD","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0305\/9482\/6376\/files\/logo_ab6f87f6-feaf-40fc-93a9-3ba98bf7db67.png?v=1769379577","url":"https:\/\/afsbio.com\/products\/etfa-monoclonal-antibody-bt-mca2018","provider":"AFSBio Inc.","version":"1.0","type":"link"}