{"product_id":"fh-fumarase-rabbit-pab-ea022","title":"FH\/Fumarase Rabbit pAb - EA022","description":"\u003cp\u003eFH\/Fumarase Rabbit pAb\u003c\/p\u003e\n\n\u003cp\u003eSizes: 50μL, 100μL\u003c\/p\u003e\n\n\u003cp\u003eCatalogue Numbers: EA022-50, EA022-100\u003c\/p\u003e\n\n\u003cp\u003eCitations, Manuals and MSDS Available upon request.\u003c\/p\u003e\n\n\u003cp\u003eBackground: Fumarase (FH) is an enzyme that catalyzes the reversible hydration\/dehydration of fumarate to malate in the mitochondria. Fumarase deficiency is caused by a mutation in the fumarase gene in humans. Fumarase deficiency is one of the few known deficiencies of the Krebs cycle or tricarboxylic acid cycle, the main enzymatic pathway of cellular aerobic respiration.\u003c\/p\u003e\n\n\u003cp\u003eAlternate Name: Fumarase, fumarate hydratase, HLRCC, LRCC, MCL, MCUL1\u003c\/p\u003e\n\n\u003cp\u003eSource: Rabbit\u003c\/p\u003e\n\n\u003cp\u003eApplications: WB, IF\u003c\/p\u003e\n\n\u003cp\u003eDilution: WB 1:1, 000\u003c\/p\u003e\n\n\u003cp\u003eReactivity: Human, Rat, Mouse\u003c\/p\u003e\n\n\u003cp\u003eImmunogen: Recombinant Protein\u003c\/p\u003e\n\n\u003cp\u003eStorage and Stability: PBS with 0.02% sodium azide and 50% glycerol pH 7.4. Store at -20°C. Avoid repeated freeze-thaw cycles.\u003c\/p\u003e\n\n\u003cp\u003eClonality: Polyclonal\u003c\/p\u003e\n\n\u003cp\u003eIsotype: IgG\u003c\/p\u003e\n\n\u003cp\u003eConcentration: 1mg\/mL\u003c\/p\u003e\n\n\u003cp\u003eObserved Band (KD): 50kDa\u003c\/p\u003e\n\n\u003cp\u003eHuman Gene ID: 2271\u003c\/p\u003e\n\n\u003cp\u003eHuman SWISS Prot NO: P07954\u003c\/p\u003e\n\n\u003cp\u003eResearch Use Only\u003c\/p\u003e","brand":"ELK Bio","offers":[{"title":"50μL","offer_id":45201791254707,"sku":"EA022-50","price":207.2,"currency_code":"CAD","in_stock":true},{"title":"100μL","offer_id":45201791287475,"sku":"EA022-100","price":347.2,"currency_code":"CAD","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0305\/9482\/6376\/files\/download_360x_b6421330-6cdd-4924-845c-981ac7f56339.png?v=1767111902","url":"https:\/\/afsbio.com\/products\/fh-fumarase-rabbit-pab-ea022","provider":"AFSBio Inc.","version":"1.0","type":"link"}