{"product_id":"fxn-frataxin-rabbit-pab-a11785","title":"FXN \/ Frataxin Rabbit pAb - A11785","description":"FXN \/ Frataxin Rabbit pAb\n\nSizes: 20μL, 100μL\n\nCatalogue Numbers: A11785-20, A11785-100\n\nCitations, Manuals and MSDS Available upon request.\n\nBackground: This nuclear gene encodes a mitochondrial protein which belongs to the FRATAXIN family. The protein functions in regulating mitochondrial iron transport and respiration. The expansion of intronic trinucleotide repeat GAA from 8-33 repeats to \u0026gt;90 repeats results in Friedreich ataxia. Alternative splicing results in multiple transcript variants.\n\nCategory: Polyclonal Antibodies\n\nApplications: WB, IHC-P, IF\/ICC, ELISA\n\nCross-reactivity: Human, Mouse, Rat\n\nProtein Weight: 23kDa\n\nObserved Molecular Weight: 19kDa\n\nImmunogen: Recombinant protein (or fragment)\n\nSpecies: Human\n\nGeneID: 2395\n\nSWISS: Q16595\n\nAlternate Names: FA; X25; CyaY; FARR; FRDA; FXN \/ Frataxin\n\nSource: Rabbit\n\nIsotype: IgG\n\nPurity: Affinity purification\n\nStorage: Store at -20℃. Avoid freeze \/ thaw cycles. Buffer: PBS containing 50% glycerol, preserved with proclin300 or sodium azide (as specified on the Certificate of Analysis),  pH 7.3.\n\nRecommended Dilutions: WB, 1:500 - 1:1000 IHC-P, 1:50 - 1:200 IF\/ICC, 1:50 - 1:200 ELISA, Recommended starting concentration is 1 μg\/mL. Please optimize the concentration based on your specific assay requirements.\n\nResearch Areas: Signal Transduction, Endocrine Metabolism, Mitochondrial metabolism, Mitochondrial markers.\n\nNCBI Alias: FXN\n\nResearch Use Only","brand":"ABclonal","offers":[{"title":"20uL","offer_id":45189507219635,"sku":"A11785-20","price":151.2,"currency_code":"CAD","in_stock":true},{"title":"100uL","offer_id":45189507252403,"sku":"A11785-100","price":417.2,"currency_code":"CAD","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0305\/9482\/6376\/files\/download_d50135fb-f719-4538-86d6-1f669bab0155.png?v=1766428576","url":"https:\/\/afsbio.com\/products\/fxn-frataxin-rabbit-pab-a11785","provider":"AFSBio Inc.","version":"1.0","type":"link"}