{"product_id":"l2hgdh-polyclonal-antibody-e-ab-63179","title":"L2HGDH Polyclonal Antibody - E-AB-63179","description":"\u003cp\u003eL2HGDH Polyclonal Antibody\u003c\/p\u003e\n\n\u003cp\u003eSizes: 60μL, 120μL, 200μL\u003c\/p\u003e\n\n\u003cp\u003eCatalogue Numbers: E-AB-63179-60, E-AB-63179-120, E-AB-63179-200\u003c\/p\u003e\n\n\u003cp\u003eCitations, Manuals and MSDS Available upon request.\u003c\/p\u003e\n\n\u003cp\u003eAbbreviation: L2HGDH\u003c\/p\u003e\n\n\u003cp\u003eTarget Synonym: L2HGDH; C14orf160; L2HGA\u003c\/p\u003e\n\n\u003cp\u003eResearch Areas: Cancer,Cell Biology,Metabolism,Signal Transduction\u003c\/p\u003e\n\n\u003cp\u003eConjugation: Unconjugated\u003c\/p\u003e\n\n\u003cp\u003eHost: Rabbit\u003c\/p\u003e\n\n\u003cp\u003eSpecies Reactivity: Human, Mouse\u003c\/p\u003e\n\n\u003cp\u003eApplication: WB\u003c\/p\u003e\n\n\u003cp\u003eIsotype: IgG\u003c\/p\u003e\n\n\u003cp\u003eClonality: Polyclonal\u003c\/p\u003e\n\n \n\n\u003cp\u003eUNIProt ID: Q9H9P8\u003c\/p\u003e\n\n\u003cp\u003eBackground: This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation.\u003c\/p\u003e\n\n\u003cp\u003eConcentration: 1 mg\/mL\u003c\/p\u003e\n\n\u003cp\u003eImmunogen: Recombinant fusion protein of human L2HGDH\u003c\/p\u003e\n\n\u003cp\u003eBuffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.\u003c\/p\u003e\n\n\u003cp\u003ePurification Method: Affinity purification\u003c\/p\u003e\n\n\u003cp\u003eDilution: WB 1:500-1:2000\u003c\/p\u003e\n\n\u003cp\u003eCalculated MW: 48kDa\/50kDa\u003c\/p\u003e\n\n\u003cp\u003eObserved MW: 40kDa\u003c\/p\u003e\n\n\u003cp\u003eStorage: -20°C\/One year. Avoid freeze \/ thaw cycles.\u003c\/p\u003e\n\n\u003cp\u003eShipping: Ice bag\u003c\/p\u003e\n\n\u003cp\u003eResearch Use Only\u003c\/p\u003e","brand":"Elabscience","offers":[{"title":"60μL","offer_id":43146278764723,"sku":"E-AB-63179-60","price":280.0,"currency_code":"CAD","in_stock":true},{"title":"120μL","offer_id":43146278797491,"sku":"E-AB-63179-120","price":448.0,"currency_code":"CAD","in_stock":true},{"title":"200μL","offer_id":43146278830259,"sku":"E-AB-63179-200","price":742.0,"currency_code":"CAD","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0305\/9482\/6376\/products\/logo_new_c2226912-702c-42a9-b383-cdfd431acf1d.png?v=1710292904","url":"https:\/\/afsbio.com\/products\/l2hgdh-polyclonal-antibody-e-ab-63179","provider":"AFSBio Inc.","version":"1.0","type":"link"}