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CLCN1 Polyclonal Antibody - RA31675

CLCN1 Polyclonal Antibody - RA31675

Regular price $336.00 CAD
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CLCN1 Polyclonal Antibody

Sizes: 50μL, 100μL

Catalogue Numbers: RA31675-50, RA31675-100

Citations, Manuals and MSDS Available upon request.

Background: chloride voltage-gated channel 1 (CLCN1) Homo sapiens The CLCN family of voltage-dependent chloride channel genes comprises nine members (CLCN1-7, Ka and Kb) which demonstrate quite diverse functional characteristics while sharing significant sequence homology. The protein encoded by this gene regulates the electric excitability of the skeletal muscle membrane. Mutations in this gene cause two forms of inherited human muscle disorders: recessive generalized myotonia congenita (Becker) and dominant myotonia (Thomsen) . Alternative splicing results in multiple transcript variants. [provided by RefSeq, Mar 2012],

Condition: Liquid in PBS containing 50% glycerol, and 0.02% sodium azide.

Storage Instructions: -20°C/1 year

Recommended dilutions: WB 1:500-2000 ELISA 1:5000-20000

Applications: WB; ELISA

Species Cross-Reactivity: Human; Rat; Mouse

GeneID (Human): 1180

Protein MW (KDa): 108

SWISS: P35523

Source: Rabbit

Research Use Only

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