WE DO NOT SHIP TO RESIDENTIAL ADDRESSES. For pricing in CAD/AUD/NZD please contact us.

L2HGDH Polyclonal Antibody - E-AB-63179

L2HGDH Polyclonal Antibody - E-AB-63179

Regular price
$280.00
Regular price
Sale price
$280.00
Unit price
per 
Availability
Sold out

L2HGDH Polyclonal Antibody

Sizes: 60μL, 120μL, 200μL

Catalogue Numbers: E-AB-63179-60, E-AB-63179-120, E-AB-63179-200

Citations, Manuals and MSDS Available upon request.

Abbreviation: L2HGDH

Target Synonym: L2HGDH; C14orf160; L2HGA

Research Areas: Cancer,Cell Biology,Metabolism,Signal Transduction

Conjugation: Unconjugated

Host: Rabbit

Species Reactivity: Human, Mouse

Application: WB

Isotype: IgG

Clonality: Polyclonal

UNIProt ID: Q9H9P8

Background: This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation.

Concentration: 1 mg/mL

Immunogen: Recombinant fusion protein of human L2HGDH

Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Purification Method: Affinity purification

Dilution: WB 1:500-1:2000

Calculated MW: 48kDa/50kDa

Observed MW: 40kDa

Storage: -20°C/One year. Avoid freeze / thaw cycles.

Shipping: Ice bag

Research Use Only