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Galactosidase alpha Recombinant Rabbit Monoclonal Antibody - BS46465
Galactosidase alpha Recombinant Rabbit Monoclonal Antibody - BS46465
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Galactosidase alpha Recombinant Rabbit mAb
Sizes: 50μl, 100μl
Catalogue Numbers: BS46465-50, BS46465-100
Lead times: 1-2 weeks, if manufacturer has product in stock
Manufacturer/Ship Location: China
Background: This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that resμlts from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jμl 2008]
Category: Primary Antibody
Reactivity: Human
Host: Rabbit
Applications: WB, IHC, ICC/IF, FC, IP
Alternate Names: GALA
Clonality: Monoclonal
Conjugate: Unconjugated
Modification: Unmodification
Immunogen: A synthetic peptide of human Galactosidase alpha
Dilution: WB: 1:1000 IHC: 1:20 ICC/IF: 1:50 FC: 1:20 IP: 1:20
Purification: Affinity Purification
Specificity: IgG
Molecular Weight: 49 kDa
Storage and Stability: Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
SwissProt: P06280
Product: Store at -20°C. Supplied in 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt.
Research Use Only
