MCCC1 Rabbit pAb - A10020

MCCC1 Rabbit pAb

Sizes: 20μL, 100μL

Catalogue Numbers: A10020-20, A10020-100

Citations, Manuals and MSDS Available upon request.

Background: This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.

Category: Polyclonal Antibodies

Applications: WB, IHC-P, ELISA

Cross-reactivity: Human, Mouse, Rat

Protein Weight: 80kDa

Observed Molecular Weight: 726aa/80kDa

Immunogen: Recombinant protein (or fragment)

Species: Human

GeneID: 56922

SWISS: Q96RQ3

Alternate Names: MCCA; MCC-B; MCCCalpha; MCCC1

Source: Rabbit

Isotype: IgG

Purity: Affinity purification

Storage: Store at -20℃. Avoid freeze / thaw cycles. Buffer: PBS containing 50% glycerol, preserved with proclin300 or sodium azide (as specified on the Certificate of Analysis),  pH 7.3.

Recommended Dilutions: WB, 1:1000 - 1:5000 IHC-P, 1:50 - 1:100 ELISA, Recommended starting concentration is 1 μg/mL. Please optimize the concentration based on your specific assay requirements.

Research Areas: Signal Transduction, Endocrine Metabolism, Mitochondrial metabolism, Mitochondrial markers, Amino acid metabolism.

NCBI Alias: MCCC1

Research Use Only