CLN6 Polyclonal Antibody - BT-AP01988

CLN6 Polyclonal Antibody

Sizes: 20μL, 50μL, 100μL

Catalogue Numbers: BT-AP01988-20, BT-AP01988-50, BT-AP01988-100

Citations, Manuals and MSDS Available upon request.

Background: CLN6 (ceroid-lipofuscinosis, neuronal 6, late infantile, variant) is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.

Research Areas: Others

Target Protein: CLN6

Applications: WB, IHC-p, ELISA

Reactivity: Human

Clonality: Polyclonal

Host: Rabbit

Isotype: IgG

Full Product Name: CLN6 Antibody

Immunogen: The antiserum was produced against synthesized peptide derived from human AMPK alpha around the phosphorylation site of Thr172. AA range:140-189

Storage: -20°C for 1 year

Purification: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.

Formulation: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.

Concentration: 1 mg/ml

Molecular Weight (Da): 35919

UniProt Accession: Human: Q9NWW5

Synonyms: CLN6; Ceroid-lipofuscinosis neuronal protein 6; Protein CLN6

GeneID: Human: 54982

Research Use Only