Product Description

ECHA Rabbit Polyclonal Antibody

Sizes: 50μL, 100μL

Catalogue Numbers: RA32112-50, RA32112-100

Lead times: 1-2 weeks, if manufacturer has product in stock

Manufacturer/Ship Location: China

Background: This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. [provided by RefSeq, Jul 2008],

Reactivity: Human, Mouse, Rat

Host: Rabbit

Applications: WB

Alternate Names: Trifunctional enzyme subunit alpha, mitochondrial (78 kDa gastrin-binding protein) (TP-alpha) [Includes: Long-chain enoyl-CoA hydratase (EC 4.2.1.17), Long chain 3-hydroxyacyl-CoA dehydrogenase (EC 1.1.1.211)]

Clonality: Polyclonal

Dilution: WB 1:500-2000

Molecular Weight: 85

Protein Molecular Weight (kDa): 85

Storage: -20°C/1 year

Human Gene ID: 3030

Human SwissProt Number: P40939

Condition: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.301% sodium azide.

Research Use Only