ECHA Rabbit Polyclonal Antibody - RA32112

ECHA Rabbit Polyclonal Antibody

Sizes: 50μL, 100μL

Catalogue Numbers: RA32112-50, RA32112-100

Citations, Manuals and MSDS Available upon request.

Background: This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. [provided by RefSeq, Jul 2008],

Condition: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.301% sodium azide.

Storage Instructions: -20°C/1 year

Recommended dilutions: WB 1:500-2000

Alternative Names: Trifunctional enzyme subunit alpha, mitochondrial (78 kDa gastrin-binding protein) (TP-alpha) [Includes: Long-chain enoyl-CoA hydratase (EC 4.2.1.17) ; Long chain 3-hydroxyacyl-CoA dehydrogenase (EC 1.1.1.211) ]

Applications: WB

Species Cross-Reactivity: Human; Mouse; Rat

GeneID (Human): 3030

Protein MW (KDa): 85

SWISS: P40939

Source: Rabbit

Research Use Only