FH/Fumarase Rabbit pAb - EA022

FH/Fumarase Rabbit pAb

Sizes: 50μL, 100μL

Catalogue Numbers: EA022-50, EA022-100

Citations, Manuals and MSDS Available upon request.

Background: Fumarase (FH) is an enzyme that catalyzes the reversible hydration/dehydration of fumarate to malate in the mitochondria. Fumarase deficiency is caused by a mutation in the fumarase gene in humans. Fumarase deficiency is one of the few known deficiencies of the Krebs cycle or tricarboxylic acid cycle, the main enzymatic pathway of cellular aerobic respiration.

Alternate Name: Fumarase, fumarate hydratase, HLRCC, LRCC, MCL, MCUL1

Source: Rabbit

Applications: WB, IF

Dilution: WB 1:1, 000

Reactivity: Human, Rat, Mouse

Immunogen: Recombinant Protein

Storage and Stability: PBS with 0.02% sodium azide and 50% glycerol pH 7.4. Store at -20°C. Avoid repeated freeze-thaw cycles.

Clonality: Polyclonal

Isotype: IgG

Concentration: 1mg/mL

Observed Band (KD): 50kDa

Human Gene ID: 2271

Human SWISS Prot NO: P07954

Research Use Only