Galactosidase alpha Monoclonal Antibody-MB10953

Galactosidase alpha Monoclonal Antibody

Sizes: 50µl, 100µl

Catalogue Numbers: MB10953-50, MB10953-100

Product: 50mM Tris-Glycine(pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% Sodium azide and 0.05% BSA

Swiss-Prot: P06280

Host: Rabbit

Reactivity: Human

Applications: WB, IHC-P, IP,

All Applications: WB: 1/500-1/1000 IHC: 1/50-1/100 IP: 1/20

Background: Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism.

Purification and Purity: Affinity Purified

Storage and Stability: Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.

Specificity: IgG

Bioworld Molecular Weight: Calculated MW: 49 kDa; Observed MW: 49 kDa

Note: For research use only, not for use in diagnostic procedure.

Extra Notes: Western blot analysis of Galactosidase alpha in K562 lysates using Galactosidase alpha antibody., Immunohistochemistry analysis of paraffin-embedded Human colon cancer using Galactosidase alpha antibody. High-pressure and temperature Sodium Citrate pH 6. 0 was used for antigen retrieval.

Alternative Name: Alpha gal A; GALA; Galactosidase; alpha; GLA; Melibiase

Immunogen: A synthetic peptide of human Galactosidase alpha

Conjugate: Unconjugated

Modification: Unmodified