LYAG Rabbit Polyclonal Antibody - BT-AP03502

LYAG Rabbit Polyclonal Antibody

Sizes: 20μL, 50μL, 100μL

Catalogue Numbers: BT-AP03502-20, BT-AP03502-50, BT-AP03502-100

Citations, Manuals and MSDS Available upon request.

Background: This gene encodes lysosomal alpha-glucosidase| which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II| also known as Pompeandapos;s disease| which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants.

Research Areas: Metabolism; Signal transduction

Target Protein: GAA

Applications: WB

Reactivity: Human, Mouse, Rat

Clonality: Polyclonal

Host: Rabbit

Isotype: IgG

Full Product Name: LYAG

Immunogen: The antiserum was produced against synthesized peptide derived from human AMPK alpha around the phosphorylation site of Thr172. AA range:140-189

Storage: -20°C for 1 year

Purification: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.

Formulation: Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.

Concentration: 1 mg/ml

UniProt Accession: Human: P10253; Mouse: P70699; Rat: Q6P7A9

Synonyms: LYAG; Lysosomal alpha-glucosidase; EC 3.2.1.20; Acid maltase; Aglucosidase alfa; 76 kDa lysosomal alpha-glucosidase; 70 kDa lysosomal alpha-glucosidase;

GeneID: Human: 2548; Mouse: 14387; Rat: 367562

Research Use Only