OTC rabbit pAb - ES14359

OTC rabbit pAb

Sizes: 50μL, 100μL

Catalogue Numbers: ES14359-50, ES14359-100

Citations, Manuals and MSDS Available upon request.

Background: This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. [provided by RefSeq, Jul 2008],

Alternate Name: Ornithine carbamoyltransferase, mitochondrial (EC 2.1.3.3) (Ornithine transcarbamylase) (OTCase)

Source: Rabbit

Applications: WB

Dilution: WB 1:500-2000

Reactivity: Human; Mouse; Rat

Immunogen: Synthesized peptide derived from human OTC AA range: 275-325

Storage and Stability: -20°C/1 year

Clonality: Polyclonal

Isotype: IgG

Concentration: 1 mg/ml

Observed Band (KD): 38kD

Human Gene ID: 5009

Human SWISS Prot NO: P00480

Subcellular Location: Mitochondrion matrix.

Research Use Only