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L2HGDH Polyclonal Antibody - E-AB-66456

L2HGDH Polyclonal Antibody - E-AB-66456

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L2HGDH Polyclonal Antibody

Sizes: 60μL, 120μL, 200μL

Catalogue Numbers: E-AB-66456-60, E-AB-66456-120, E-AB-66456-200

Citations, Manuals and MSDS Available upon request.

Abbreviation: L2HGDH

Target Synonym: L2HGDH; C14orf160; L2HGA

Research Areas: Cancer, Cell Biology, Metabolism, Signal Transduction

Conjugation: Unconjugated

Host: Rabbit

Species Reactivity: Human, Mouse

Application: IF

Isotype: IgG

Clonality: Polyclonal

UNIProt ID: Q9H9P8

Background: This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation.

Concentration: 1mg/mL

Immunogen: Recombinant fusion protein of human L2HGDH (NP_079160.1).

Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Purification Method: Affinity purification

Dilution: IF 1:50-1:200

Storage: -20°C/One year. Avoid freeze / thaw cycles.

Shipping: Ice bag

Research Use Only