PAH Rabbit mAb
Sizes: 20µl, 100µl
Catalogue Numbers: A20949-20, A20949-100
Citations, Manuals and SDS Available upon request.
Background: This gene encodes a member of the biopterin-dependent aromatic amino acid hydroxylase protein family. The encoded phenylalanine hydroxylase enzyme hydroxylates phenylalanine to tyrosine and is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria.
Synonyms: PH; PKU; PKU1; PAH
GeneID: 5053
Swiss-Prot: P00439
Reactivity: Human, Mouse, Rat
Tested Applications: ELISA, WB, IF/ICC
Calculated Molecular Weight: 52kDa
Observed Molecular Weight: 52kDa
Immunogen: A synthetic peptide corresponding to a sequence within amino acids 1-100 of human PAH (P00439).
Immunogen Species: Human
Host: Rabbit
Isotype: IgG
Purity: Affinity purification
Storage Buffer: Store at -20℃. Avoid freeze / thaw cycles. Buffer: PBS with 0.02% sodium azide, 0.05% BSA, 50% glycerol, pH7.3.
Research Areas: Signal Transduction, Endocrine Metabolism, Amino acid metabolism
Recommended Dilutions: WB: 1:100 - 1:500 | IF/ICC: 1:50 - 1:200
Modifications: Unmodified
Conjugate: Unconjugated
Cellular Location: Cytosol
Positive Samples: HepG2, Mouse liver, Mouse kidney, Rat liver
Keywords: 5053, sc-15109, sc-15112, PAH, PH, PKU, PKU1, phenylalanine hydroxylase, phenylalanine-4-hydroxylase, phe-4-monooxygenase, phenylalanine 4-monooxygenase, P00439, Phenylalanine Hydroxylase, Phenylalanine 4-Monooxygenase, Phe-4-Monooxygenase, Phenylalanine-4-Hydroxylase, EC 1.14.16.1, sc15109, sc 15109, sc15112, sc 15112, Phe 4 monooxygenase, Phenylalanine 4 hydroxylase
Symbol: PAH
Category: Monoclonal Antibodies
Research Use Only